KBB-Forum 2004 , Cilt 3, Sayı 2

PRIMARY SUBMANDIBULARY GLAND LYMPHOMA IN A PATIENT WITH ATAXIA TELENJIEKTAZIA:CASE REPORT

Dr. Köksal YUCA1, Dr. Hakan ÇANKAYA1, Dr. A. Faruk KIROĞLU1, Dr. Süleyman ALICI2, Dr. Ferhat BOZKUŞ1
Dr. Ahmet KUTLUHAN1
1Yüzüncüyıl Üniversitesi, KBB ABD, Van, Türkiye
2Yüzüncüyıl Üniversitesi, Medikal Onkoloji, Van, Türkiye Ataxia Telenjiektazia (AT, Louis- Bar syndrome) is a rare clinical syndrome that commonly shows oculocutanöz telengiectasia, progressive cerebellar ataxia, recurrent sinopulmonary infections, incresed incidence of malignancy, x-ray hypersensitivity, and autosomal recessive inheritance.

We present a 22 year old man with respiratory distress, high fever and cervical mass admitted to our clinic. The patient following by the neurology clinic with the diagnosis of A-T and mental retardation. Lymphoma of submandibular gland origin and deep neck infection was revealed. Keywords : Ataxia Telenjiektazia, Lymphoma, Submandibular gland